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This is usually sporadic, with rare instances of familial congenital naevi

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Propionyl-L-carnitine is used for treating leg pain (intermittent claudication) due to poor blood circulation (peripheral vascular disease, PVD)

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So what you have in the case of somebody who is diabetic, type 2 diabetes in particular, is you have an elevated circulating level of insulin that can't bind to its receptor, can't get the sugar into the cells, so the sugar builds up in the bloodstream

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Structure of mitochondrial ADP/ATP carrier in complex with carboxyatractyloside

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doi: 10.1111/j.1537-2995.2011.03100.x

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